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Dryad

Data from: Intra-Rater reliability and validity of outcome measures in Myotonic Dystrophy Type 1

Cite this dataset

Knak, Kirsten Lykke et al. (2020). Data from: Intra-Rater reliability and validity of outcome measures in Myotonic Dystrophy Type 1 [Dataset]. Dryad. https://doi.org/10.5061/dryad.h18931zfq

Abstract

Objective

To investigate intra-rater reliability, concurrent- and construct validity of muscle strength, balance, and functional mobility measures in individuals with non-congenital DM1.

Methods

Seventy-eight adults with non-congenital DM1 participated in visit 1 and 73 of the subjects participated in visit 2 separated by 1-2 weeks. The assessments consisted of muscle strength tests with Hand-Held Dynamometry (HHD) and Stationary Dynamometry in the lower limb. The balance tests comprised of Step Test, Timed Up and Go test, Feet-Together stance, Tandem-Stance, One-Leg-Stance, and modified Clinical Test of Sensory Integration and Balance on a balance platform. The functional mobility tests consisted of the 10-meter Walk Test (10mWT) and 10-times Sit-To-Stand test.

Results

The HHD and Stationary Dynamometry were sufficiently intra-rater reliable for most muscle groups on a group- (SEM%≤15%) and individual level (MDD95%≤30%), but HHD was most reliable. Stationary Dynamometry measured a higher torque than HHD for all extensor muscles, but for single individuals none of the devices were favored. Overall, intra-rater reliability and validity were only sufficient for the dynamic balance tests and not the static balance tests. Both functional mobility tests were sufficiently reliable and valid, but the 10mWT was most reliable.

Conclusion

Overall, HHD is recommended as a reliable and valid tool for single individuals and for flexor muscles on a group level. For balance assessments, the dynamic balance tests are recommended as the most valid and reliable balance tests. Both functional mobility tests are recommended for valid and reliable outcomes, but the 10mWT was superior for reliability.